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KMID : 1155520100050040329
Anesthesia and Pain Medicine
2010 Volume.5 No. 4 p.329 ~ p.332
General anesthesia for a spinal muscular atrophy type I patient undergoing feeding gastrostomy -A case report-
Jang Eun-Ho

Cho Kwang-Rae
Kim Hyun-Tae
Lim Se-Hun
Lee Jeong-Han
Lee Kun-Moo
Cheong Soon-Ho
Kim Young-Jae
Shin Chee-Mahn
Abstract
Spinal muscular atrophy (SMA) in children leads to progressive muscle weakness, dysphagia, aspiration, and death. The most common and severe form of SMA is designated as type I, also known as Werdnig-Hoffman Disease or Floppy Baby syndrome. We anesthetized an 8 month-old female infant with SMA type I undergoing feeding gastrostomy. We planned to use inhalational anesthesia without muscle relaxants. Anesthesia and surgery were uneventful. We herein report a case of successful peri-operative anesthetic management for SMA type I infant with aspiration pneumonia.
KEYWORD
Gastrostomy, Neuromuscular disease, Spinal muscular atrophy type I
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