KMID : 1155520100050040329
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Anesthesia and Pain Medicine 2010 Volume.5 No. 4 p.329 ~ p.332
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General anesthesia for a spinal muscular atrophy type I patient undergoing feeding gastrostomy -A case report-
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Jang Eun-Ho
Cho Kwang-Rae Kim Hyun-Tae Lim Se-Hun Lee Jeong-Han Lee Kun-Moo Cheong Soon-Ho Kim Young-Jae Shin Chee-Mahn
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Abstract
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Spinal muscular atrophy (SMA) in children leads to progressive muscle weakness, dysphagia, aspiration, and death. The most common and severe form of SMA is designated as type I, also known as Werdnig-Hoffman Disease or Floppy Baby syndrome. We anesthetized an 8 month-old female infant with SMA type I undergoing feeding gastrostomy. We planned to use inhalational anesthesia without muscle relaxants. Anesthesia and surgery were uneventful. We herein report a case of successful peri-operative anesthetic management for SMA type I infant with aspiration pneumonia.
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KEYWORD
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Gastrostomy, Neuromuscular disease, Spinal muscular atrophy type I
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